Kartagener's Syndrome

A 46-year-old man with Kartagener’s Syndrome (primary ciliary diskinesia, autosomal recessive disorder with dextrocardia, situs inversus, bronchiectasis and paranasal sinusitis) presented with new onset angina. Coronary arteriography revealed severe three-vessel disease with occluded left anterior descending and circumflex coronary arteries. Due to severe pulmonary disease, coronary artery bypass surgery was not considered as the first therapeutic option. He underwent successful percutaneous multivessel revascularisation with implantation of paclitaxel-eluting stents. Control coronary angiography nine months after the procedure revealed no signs of restenosis. The patient remains asymptomatic at two years.



Figure 1. Dual source 64 multi-slice computed tomography volume-rendered image of ...